Pesquisa sobre: METHYLMALONYL-COA DECARBOXYLASE 
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Descritor Inglês:   Methylmalonyl-CoA Decarboxylase 
Descritor Espanhol:   Metilmalonil-CoA Descarboxilasa 
Descritor Português:   Metilmalonil-CoA Descarboxilase 
Sinônimos Inglês:   Carboxylase, Propionyl-Coenzyme A
Decarboxylase, Methylmalonyl-CoA
Methylmalonyl CoA Decarboxylase
Propionyl CoA Carboxylase
Propionyl Coenzyme A Carboxylase
Propionyl-CoA Carboxylase
Propionyl-Coenzyme A Carboxylase  
Categoria:   D08.811.520.224.125.387
Definição Inglês:   A carboxy-lyase that catalyzes the decarboxylation of (S)-2-Methyl-3-oxopropanoyl-CoA to propanoyl-CoA. In microorganisms the reaction can be coupled to the vectorial transport of SODIUM ions across the cytoplasmic membrane. 
Combinados Inglês:   Methylmalonyl-CoA Decarboxylase/deficiency use Propionic Acidemia
 
Relacionados Inglês:   Propionic Acidemia
 
Nota Histórica Inglês:   2004; use METHYLMALONYL-COA DECARBOXYLASE (NM) 1980-2003 
Qualificadores Permitidos Inglês:  
AD administration & dosage AE adverse effects
AN analysis AI antagonists & inhibitors
BI biosynthesis BL blood
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
DE drug effects EC economics
GE genetics HI history
IM immunology IP isolation & purification
ME metabolism PK pharmacokinetics
PD pharmacology PH physiology
PO poisoning RE radiation effects
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Número do Registro:   38186 
Identificador Único:   D043586 

Ocorrência na BVS:
 

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